Case No. | Age (yr)/gender | Area and year of report | Abdominal symptoms | Other clinical presentations | Skin and mucous membrane appearance | Involved organ or tissue/diagnostic methods | Treatment maintenance | Outcome |
---|---|---|---|---|---|---|---|---|
1 | 72/M | Hong Kong China 1992 [4] | GI bleeding | anorexia, dysphagia, weight loss | jejunal ulcer(S) | small intestine(B + C), mesenteric lymph node, liver(A) | NM | Died |
2 | 32/M | Hong Kong China 1996 [5] | diarrhea | fever, night sweats, dry cough | multiple solitary ulcers(E) | cecum, transverse and descending colon(B + C) | Amphotericin B/Itraconazole | survived |
3、4 | NM | Thai 1998 [8] | abdominal pain | fever | NM | mesenteric lymph node (B), blood and bone marrow (C) | Amphotericin B | survived |
5 | 52/M | Taiwan China 1999 [6] | diarrhea, abdominal pain | fever, erupted papule, anomia, | shallow ulcers(E) | skin, bone marrow(B + C), colons(B) | Amphotericin B/Itraconazole | survived |
6 | 30/M | Taiwan China 1999 [6] | diarrhea, abdominal pain, bloody stool | dyspepsia, fever, anomia, weight loss | shallow ulcers(E) | cecum, ascending and transverse colons(B + C) | Amphotericin B/Itraconazole | survived |
7 | 33/M | India 2008 [7] | abdominal pain | fever, loss of appetite, weight loss, vomiting | duodenum narrowing(E) | duodenum(B + C), bone marrow(C) | Amphotericin B/Itraconazole | survived |
8 | 39/M | Hong Kong China 2010 [9] | Abdominal pain | fever, weight loss | perioral umbilicated lesions | neck and retroperitoneal lymph nodes (H + C),blood (C) | Amphotericin B/Itraconazole | Survived |
9 | 28/M | India 2014 [10] | non-colicky abdominal pain | fever, weight loss | perioral umbilicated lesions | neck nodes and retroperitoneal lymph nodes(B + C), blood(C) | Amphotericin B/Itraconazole | survived |
10 | 52/M | China 2017 [11] | pain in the lower left abdomen | anorexia, weight loss | multiple solitary shallow ulcers (E) | transverse colon (B + H) | Itraconazole | survived |
11 | 38/F | India 2020 [12] | colicky abdominal pain | loss of appetite, weight loss | skin lesions, jejunal ulcers(E) | skin, jejunal ulcers(B + C), | Amphotericin B/Itraconazole | survived |
12 | 37/M | China 2020 [13] | Abdominal pain | NM | multiple ulcers (E) | colon (B), blood (C) | Amphotericin B/Itraconazole | Survived |
13 | 50/M | China 2020 [13] | Abdominal pain | weight loss | multiple ulcers (E) | colon (B) | Voriconazole+Amphotericin B/Itraconazole | Survived |
14 | 33/M | China [PR] | colicky abdominal pain, bloody stool | fever, weight loss, night sweats | colon ulcers(E) | Mesenteric lymph node(B + N) | Amphotericin B/Itraconazole | survived |