Infectious Diseases (out of 1197 cases from 18 case-series where details are available)
|
Mycobacterial diseases
|
440 (36.8%)
|
17
|
Endocarditis
|
119 (9.9%)
|
15
|
Brucellosis
|
58 (4.8%)
|
9
|
Internal abscesses
|
49 (4.1%)
|
11
|
Salmonellosis
|
43 (3.6%)
|
9
|
CMV infections
|
43 (3.6%)
|
7
|
Urinary tract infections
|
40 (3.3%)
|
11
|
Sepsis
|
20 (1.7%)
|
4
|
HIV/AIDS
|
20 (1.7%)
|
4
|
Osteoarticular infections
|
18 (1.5%)
|
5
|
Neoplasms (out of 289 cases from 15 case-series where details are available)
|
Lynphomas (including Hodgkin, Non-Hodgkin, not specified)
|
169 (58.5%)
|
9
|
Solid tumors (not specified)
|
25 (8.7%)
|
4
|
Leukemias
|
17 (5.9%)
|
7
|
Other cancers (not specified)
|
14 (4.8%)
|
5
|
Myelodysplastic syndrome
|
11 (3.8%)
|
7
|
Colon cancers
|
10 (3.5%)
|
5
|
Multiple mieloma
|
8 (2.8%)
|
6
|
Gastric cancers
|
5 (1.7%)
|
3
|
Mesotheliomas
|
5 (1.7%)
|
3
|
Castleman’s diseases
|
4 (1.4%)
|
3
|
NIIDs (out of 642 cases from 17 case-series where details are available)
|
Adult-onset Still’s disease
|
177 (27. 6%)
|
15
|
Systemic Lupus Erythematosus
|
71 (11.1%)
|
14
|
Vasculitis
|
63 (9.8%)
|
8
|
Rheumatic Polymyalgia
|
44 (6.9%)
|
8
|
Giant Cells Arteritis
|
32 (5.0%)
|
6
|
Mixed connective diseases (not specified)
|
31 (4.8%)
|
5
|
Sarcoidosis
|
21 (3.3%
|
7
|
Rheumatoid Arthritis
|
17 (2.6%)
|
6
|
Wegener Granulomatosis
|
14 (2.2%)
|
4
|
Polyarteritis nodosa
|
13 (2.0%)
|
5
|