From: Debate around infection-dependent hemophagocytic syndrome in paediatrics
Type of hemophagocytic syndrome | Subtype |
---|---|
Primary or genetic hemophagocytic syndrome | Familial hemophagocytic lymphohistiocytosis |
 | Immune deficiency syndromes (i.e., Chediak-Higashi syndrome, Griscelli syndrome, X-linked lymphoproliferative syndrome) |
Secondary or reactive hemophagocytic syndrome | Infections (i.e., viral, bacterial, parasitic) |
 | Malignancies |
 | Auto-immune and auto-inflammatory diseases |