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Table 1 Classification of hemophagocytic syndrome

From: Debate around infection-dependent hemophagocytic syndrome in paediatrics

Type of hemophagocytic syndrome

Subtype

Primary or genetic hemophagocytic syndrome

Familial hemophagocytic lymphohistiocytosis

 

Immune deficiency syndromes (i.e., Chediak-Higashi syndrome, Griscelli syndrome, X-linked lymphoproliferative syndrome)

Secondary or reactive hemophagocytic syndrome

Infections (i.e., viral, bacterial, parasitic)

 

Malignancies

 

Auto-immune and auto-inflammatory diseases